Abstract: The authors reported a case of inflammatory myofibroblastic tumor (IMT) of the right parietal bone. The characteristics of the disease were analyzed on the basis of clinical symptoms, imaging findings, laboratory examinations and pathological diagnosis results. IMT is rare to occur in the parietal bone, both the clinical manifestations and imaging findings are non-specific. The imaging features and differential diagnosis methods of the disease were summarized combined with literature review, aiming to improve the understanding and diagnostic ability of the disease.