Abstract: Limb weakness was presented as the first symptom. This work analyzes the characteristics of the patient based on clinical symptoms, related laboratory tests, CT, and ¹⁸F-FDG and ⁶⁸Ga-1, 4, 7, 10-tetraazacyclododecane-N, N, N, N-tetraacetic acid-D-Phe1-Tyr3-Thr8-octreotide (⁶⁸Ga-DOTATATE) PET/CT and reviewed the imaging diagnosis methods of primary pulmonary NK/T cell lymphoma. Considering the low incidence of the disease, this study suggests that imaging physicians should understand the whole situation when encountering similar cases and avoid preconceived thinking to improve the diagnostic level.