Abstract: Ovarian granulosa cell tumor (OGCT) and alveolar soft part sarcoma (ASPS) are relatively rare in clinical practice, especially in the presence of both tumors. The prognosis of OGCT is fair, but the prognosis of ASPS is not optimistic, and there are few reports of ¹⁸F-fluorodeoxyglucose (FDG) PET/CT of OGCT and ASPS at present. The author reported the whole body ¹⁸F-FDG PET/CT imaging and MRI of a patient with OGCT accompanied by lung metastasis and left thigh ASPS, analyzed the image characteristics and reviewed the literature to provide more reference for the diagnosis of this disease.