Abstract: A case of rib hemangioma was reported. The characteristics of the disease were analyzed including the clinical symptoms, imaging manifestations, clinical diagnosis, pathological diagnosis and histopathological, and were deepened the understanding through literature review. The case was confirmed as rib hemangioma by the pathology. The disease progresses relatively slowly and had low specificity in the imaging. It was not only diagnosed by histopathological, but the imaging findings still have some value in this disease. The imaging manifestations of the disease are varied, which are easy to be confused with malignant bone tumors and bone tumor-like lesions. Once myofibroblastoma occurs, it is easy to misdiagnose. Thus, a combination of clinical symptoms, imaging manifestations, postoperative histopathological and therapeutic considerations is needed.