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脊索瘤起源于原始胚胎脊索组织,好发于人体中轴骨,尤其是颅底及骶尾的区域。笔者报道了1例发生于右侧鼻腔-筛窦的脊索瘤,旨在增加对发生在罕见部位脊索瘤的认识,为临床治疗提供参考。
右侧鼻腔-筛窦脊索瘤CT 和MRI 影像学表现一例
CT and MRI imaging features of right nasal ethmoid chordoma: a case report
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摘要: 脊索瘤好发于中轴骨,以颅底及骶尾区域最为常见,发生在其他部位较罕见。笔者报道了1例经组织病理学检查结果证实的发生在右侧鼻腔-筛窦的脊索瘤病例,分别从临床症状、术前CT及MRI影像学表现、手术所见及术后组织病理学、免疫组织化学检查结果分析了该病的特点,并通过文献复习鉴别诊断,加深了对该病的认识,为临床诊断及治疗方式提供有价值的参考。Abstract: Chordomas mainly occur in the axial bones, the most common in the base of the skull and the sacrococcygeal region, and are rare in other parts. The author reported a case of chordoma in the right nasal cavity and ethmoid sinus confirmed by histopathological results. The clinical symptoms, preoperative CT and MRI imaging findings, surgical findings and postoperative histopathology immunohistochemical examination results were analyzed. The characteristics of the disease and the differential diagnosis through literature review have deepened the understanding of the disease, provide valuable reference for clinical diagnosis and treatment.
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